Myositis
- General information
- Criteria and Outcome Measures
- Disease Scores and Online Calculators
- Patient Organisations
- Recommendations and Guidelines
- Scales and Questionnaires
General information
Take a look at the following links from Orphanet about the different types of myositis.
- Focal myositis: https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=EN&Expert=48918
- Polymyositis: https://www.orpha.net/consor/cgi-bin/OC_Exp.php?Expert=732
- Inclusion body myositis: https://www.orpha.net/consor/cgi-bin/OC_Exp.php?Lng=EN&Expert=611
- Overlap myositis: https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=EN&Expert=206572
- Dermatomyositis: https://www.orpha.net/consor/cgi-bin/OC_Exp.php?Lng=GB&Expert=221
- Juvenile dermatomyositis: https://www.orpha.net/consor/cgi-bin/OC_Exp.php?Lng=EN&Expert=93672
- Antisynthetase syndrome: https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=EN&Expert=81
More information about the diagnosis and treatment of antisynthetase syndrome can be found here.
Criteria and Outcome Measures
1975 Bohan and Peter criteria
(The New England Journal of Medicine 292: 403-7)
http://www.nejm.org/doi/full/10.1056/NEJM197502202920807
1995 Griggs criteria for Inclusion Body Myositis
(Annals of Neurology 38: 705-13.)
http://onlinelibrary.wiley.com/doi/10.1002/ana.410380504/full
2014 Evaluation and construction of diagnostic criteria for inclusion body myositis.
(Neurology 29; 83(5): 426–433.)
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4132572/
2016 American College of Rheumatology/European League Against Rheumatism Criteria for Minimal, Moderate, and Major Clinical Response in Adult Dermatomyositis and Polymyositis: An International Myositis Assessment and Clinical Studies Group/Paediatric Rheumatology International Trials Organisation Collaborative Initiative.
(Arthritis & Rheumatology 69(5): 898-910)
http://onlinelibrary.wiley.com/doi/10.1002/art.40064/abstract;jsessionid=F5B0AA4562E94E743A62C6AB25A4290E.f02t01
2017 Classification of Adult Autoimmune Myositis
(Arthritis & Rheumatology 69(5): 878-884.
http://onlinelibrary.wiley.com/doi/abs/10.1002/art.40063
Disease Scores and Online Calculators
Scores and online calculators for juvenile myositis
Childhood Myositis Assessment Scale (CMAS)
Arthritis & Rheumatism. 2014: 50: 1595–1603.
http://onlinelibrary.wiley.com/doi/10.1002/art.20179/abstract
Disease activity score for Juvenile Dermatomyositis
Arthritis Rheum. 2003 Feb 15;49(1):7-15.
http://onlinelibrary.wiley.com/doi/10.1002/art.10924/abstract
Scores and online calculators for adult myositis
Classification Criteria for Idiopathic Inflammatory Myopathies
Intern Med. 2016; 280:39–51.
http://www.imm.ki.se/biostatistics/calculators/iim/
Cutaneous Assessment Tool (CAT)
Arthritis Rheum. 2008 Mar 15;59(3): 352–356.
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2598766/
Rheumatology (Oxford). 2007 46(10):1606-11
http://www.ncbi.nlm.nih.gov/pubmed?term=PMID%3A%2017890275
Dermatomyositis Skin Severity Index (DSSI)
Br J Dermatol 2008;158:345–50
http://onlinelibrary.wiley.com/doi/10.1111/j.1365-2133.2007.08342.x/abstract
Modified Cutaneous Dermatomyositis Disease Area and Severity Index (CDASI)
Br J Dermatol 2010;162:669-73
http://onlinelibrary.wiley.com/doi/10.1111/j.1365-2133.2009.09521.x/abstract
Myositis Disease Activity Assessment Tool (MDAAT)
Arthritis Rheum 2008;58:3593-9 & Rheumatology (Oxford) 2004;43:49-54
http://onlinelibrary.wiley.com/doi/10.1002/art.23963/abstract
Summary of IMACS disease activity core set measures:
https://www.niehs.nih.gov/research/resources/imacs/diseaseactivity/index.cfm
Summary of IMACS disease damage core set measures:
https://www.niehs.nih.gov/research/resources/imacs/diseasedamage/index.cfm
Patient Organisations
Myositis Support Group (UK)
The Myositis Support Group is a UK charity providing advice and support to individuals and their families affected by Dermatomyositis, Polymyositis, Inclusion Body Myositis and Juvenile Dermatomyositis
http://www.myositis.org.uk
The Myositis Association
The Myositis Association provides support to myositis patients and their families, works on establishing connections with medical and patient communities and providing funding for research
http://www.myositis.org
Recommendations and Guidelines
Proposed preliminary core set measures for disease outcome assessment in adult and juvenile idiopathic inflammatory myopathies
(Rheumatology (Oxford) 2001;40:1262–73)
https://academic.oup.com/rheumatology/article/40/11/1262/1784014/Proposed-preliminary-core-set-measures-for-disease
Immunosuppressant and immunomodulatory treatment for dermatomyositis and polymyositis. Cochrane database Syst Rev 2012;8:CD003643. doi:10.1002/14651858.CD003643.pub4
http://dx.doi.org/10.1002/14651858.CD003643.pub4
The evidence for immunotherapy in dermatomyositis and polymyositis: a systematic review.
Clin Rheumatol 2015;34:2089–95. doi:10.1007/s10067-015-3059-y
https://link.springer.com/article/10.1007%2Fs10067-015-3059-y
Scales and Questionnaires
Inclusion body myositis functional rating scale: a reliable and valid measure of disease severity
Muscle Nerve 2008;37:473–6. doi:10.1002/mus.20958
http://onlinelibrary.wiley.com/doi/10.1002/mus.20958/abstract
Myositis Activities Profile (MAP)
J Rheumatol 2002;29:2386–92
http://www.jrheum.org/content/29/11/2386.long
IMACS Myositis Damage Index (MDI) (pdf form)
https://www.niehs.nih.gov/research/resources/assets/docs/myositis_damage_index_pdf_format_508.pdf
Myositis Functional Index-2 (FI-2)
Arthritis Rheum 2006;55:114–22
http://onlinelibrary.wiley.com/doi/10.1002/art.21715/abstract