Criteria & Outcome Measures

1975 Bohan and Peter criteria
(N Engl J Med 1975;292:403-7)

Griggs criteria for Inclusion Body Myositis
(Ann Neurol. 1995;38:705-13.)

Evaluation and construction of diagnostic criteria for inclusion body myositis.
(Neurology. 2014 Jul 29; 83(5): 426–433.)

2016 American College of Rheumatology/European League Against Rheumatism Criteria for Minimal, Moderate, and Major Clinical Response in Adult Dermatomyositis and Polymyositis: An International Myositis Assessment and Clinical Studies Group/Paediatric Rheumatology International Trials Organisation Collaborative Initiative.
(Arthritis Rheumatol. 2017 May;69(5):898-910);jsessionid=F5B0AA4562E94E743A62C6AB25A4290E.f02t01


Disease Scores & Online Calculators

Classification Criteria for Idiopathic Inflammatory Myopathies
Intern Med. 2016; 280:39–51.

Childhood Myositis Assessment Scale (CMAS)
Arthritis & Rheumatism. 2014: 50: 1595–1603.

Cutaneous Assessment Tool (CAT)
Arthritis Rheum. 2008 Mar 15;59(3): 352–356.

Rheumatology (Oxford). 2007 46(10):1606-11

Dermatomyositis Skin Severity Index (DSSI)
Br J Dermatol 2008;158:345–50

Disease activity score for Juvenile Dermatomyositis
Arthritis Rheum. 2003 Feb 15;49(1):7-15.

Modified Cutaneous Dermatomyositis Disease Area and Severity Index (CDASI)
Br J Dermatol 2010;162:669-73

Myositis Disease Activity Assessment Tool (MDAAT)
Arthritis Rheum 2008;58:3593-9 & Rheumatology (Oxford) 2004;43:49-54

Summary of IMACS disease activity core set measures:

Summary of IMACS disease damage core set measures:


Patient Organizations

Myositis Support Group (UK)
The Myositis Support Group is a UK charity providing advice and support to individuals and their families affected by Dermatomyositis, Polymyositis, Inclusion Body Myositis and Juvenile Dermatomyositis

The Myositis Association
The Myositis Association provides support to myositis patients and their families, works on establishing connections with medical and patient communities and providing funding for research


Recommendations & Guidelines

Proposed preliminary core set measures for disease outcome assessment in adult and juvenile idiopathic inflammatory myopathies
(Rheumatology (Oxford) 2001;40:1262–73)

Immunosuppressant and immunomodulatory treatment for dermatomyositis and polymyositis. Cochrane database Syst Rev 2012;8:CD003643. doi:10.1002/14651858.CD003643.pub4

The evidence for immunotherapy in dermatomyositis and polymyositis: a systematic review.
Clin Rheumatol 2015;34:2089–95. doi:10.1007/s10067-015-3059-y


Scales & Questionnaires

Inclusion body myositis functional rating scale: a reliable and valid measure of disease severity
Muscle Nerve 2008;37:473–6. doi:10.1002/mus.20958

Myositis Activities Profile (MAP)
J Rheumatol 2002;29:2386–92

IMACS Myositis Damage Index (MDI) (pdf form)

Myositis Functional Index-2 (FI-2)
Arthritis Rheum 2006;55:114–22