Myositis

General information

Take a look at the following links from Orphanet about the different types of myositis.

More information about the diagnosis and treatment of antisynthetase syndrome can be found here.

Criteria and Outcome Measures

1975 Bohan and Peter criteria
(The New England Journal of Medicine 292: 403-7)
http://www.nejm.org/doi/full/10.1056/NEJM197502202920807

1995 Griggs criteria for Inclusion Body Myositis
(Annals of Neurology 38: 705-13.)
http://onlinelibrary.wiley.com/doi/10.1002/ana.410380504/full

2014 Evaluation and construction of diagnostic criteria for inclusion body myositis.
(Neurology 29; 83(5): 426–433.)
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4132572/

2016 American College of Rheumatology/European League Against Rheumatism Criteria for Minimal, Moderate, and Major Clinical Response in Adult Dermatomyositis and Polymyositis: An International Myositis Assessment and Clinical Studies Group/Paediatric Rheumatology International Trials Organisation Collaborative Initiative.
(Arthritis & Rheumatology 69(5): 898-910)
http://onlinelibrary.wiley.com/doi/10.1002/art.40064/abstract;jsessionid=F5B0AA4562E94E743A62C6AB25A4290E.f02t01

2017 Classification of Adult Autoimmune Myositis
(Arthritis & Rheumatology 69(5): 878-884.
http://onlinelibrary.wiley.com/doi/abs/10.1002/art.40063

Disease Scores and Online Calculators

Scores and online calculators for juvenile myositis

Childhood Myositis Assessment Scale (CMAS)
Arthritis & Rheumatism. 2014: 50: 1595–1603.
http://onlinelibrary.wiley.com/doi/10.1002/art.20179/abstract

Disease activity score for Juvenile Dermatomyositis
Arthritis Rheum. 2003 Feb 15;49(1):7-15.
http://onlinelibrary.wiley.com/doi/10.1002/art.10924/abstract

Scores and online calculators for adult myositis

Classification Criteria for Idiopathic Inflammatory Myopathies
Intern Med. 2016; 280:39–51.
http://www.imm.ki.se/biostatistics/calculators/iim/

Cutaneous Assessment Tool (CAT)
Arthritis Rheum. 2008 Mar 15;59(3): 352–356.
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2598766/

Rheumatology (Oxford). 2007 46(10):1606-11
http://www.ncbi.nlm.nih.gov/pubmed?term=PMID%3A%2017890275

Dermatomyositis Skin Severity Index (DSSI)
Br J Dermatol 2008;158:345–50
http://onlinelibrary.wiley.com/doi/10.1111/j.1365-2133.2007.08342.x/abstract

Modified Cutaneous Dermatomyositis Disease Area and Severity Index (CDASI)
Br J Dermatol 2010;162:669-73
http://onlinelibrary.wiley.com/doi/10.1111/j.1365-2133.2009.09521.x/abstract

Myositis Disease Activity Assessment Tool (MDAAT)
Arthritis Rheum 2008;58:3593-9 & Rheumatology (Oxford) 2004;43:49-54
http://onlinelibrary.wiley.com/doi/10.1002/art.23963/abstract

Summary of IMACS disease activity core set measures:
https://www.niehs.nih.gov/research/resources/imacs/diseaseactivity/index.cfm

Summary of IMACS disease damage core set measures:
https://www.niehs.nih.gov/research/resources/imacs/diseasedamage/index.cfm

Patient Organisations

Myositis Support Group (UK)
The Myositis Support Group is a UK charity providing advice and support to individuals and their families affected by Dermatomyositis, Polymyositis, Inclusion Body Myositis and Juvenile Dermatomyositis
http://www.myositis.org.uk

The Myositis Association
The Myositis Association provides support to myositis patients and their families, works on establishing connections with medical and patient communities and providing funding for research
http://www.myositis.org

Recommendations and Guidelines

Proposed preliminary core set measures for disease outcome assessment in adult and juvenile idiopathic inflammatory myopathies
(Rheumatology (Oxford) 2001;40:1262–73)
https://academic.oup.com/rheumatology/article/40/11/1262/1784014/Proposed-preliminary-core-set-measures-for-disease

Immunosuppressant and immunomodulatory treatment for dermatomyositis and polymyositis. Cochrane database Syst Rev 2012;8:CD003643. doi:10.1002/14651858.CD003643.pub4
http://dx.doi.org/10.1002/14651858.CD003643.pub4

The evidence for immunotherapy in dermatomyositis and polymyositis: a systematic review.
Clin Rheumatol 2015;34:2089–95. doi:10.1007/s10067-015-3059-y
https://link.springer.com/article/10.1007%2Fs10067-015-3059-y

Scales and Questionnaires

Inclusion body myositis functional rating scale: a reliable and valid measure of disease severity
Muscle Nerve 2008;37:473–6. doi:10.1002/mus.20958
http://onlinelibrary.wiley.com/doi/10.1002/mus.20958/abstract

Myositis Activities Profile (MAP)
J Rheumatol 2002;29:2386–92
http://www.jrheum.org/content/29/11/2386.long

IMACS Myositis Damage Index (MDI) (pdf form)
https://www.niehs.nih.gov/research/resources/assets/docs/myositis_damage_index_pdf_format_508.pdf

Myositis Functional Index-2 (FI-2)
Arthritis Rheum 2006;55:114–22
http://onlinelibrary.wiley.com/doi/10.1002/art.21715/abstract