Recommendations & Guidelines

EULAR/ERA-EDTA recommendations for the management of ANCA-associated vasculitis.
(Ann Rheum Dis. 2016;75:1583-94.)

CanVasc Recommendations for the Management of Antineutrophil Cytoplasm Antibody-associated Vasculitides.
(J Rheumatol. 2016;43:97-120.)

BSR and BHPR guideline for the management of adults with ANCA-associated vasculitis.
(Rheumatology (Oxford). 2014;53:2306-9.)

Eosinophilic granulomatosis with polyangiitis (Churg-Strauss) (EGPA) Consensus Task Force recommendations for evaluation and management.
(Eur J Intern Med. 2015;26:545-53.)

Management of giant cell arteritis: Recommendations of the French Study Group for Large Vessel Vasculitis (GEFA).
(Rev Med Interne. 2016;37:154-65.)

BSR and BHPR guidelines for the management of giant cell arteritis.
(Rheumatology (Oxford). 2010;49:1594-7.)

EULAR recommendations for the management of large vessel vasculitis.
(Ann Rheum Dis. 2009;68:318-23.)

EULAR recommendations for the management of Behçet disease.
(Ann Rheum Dis. 2008;67:1656-62.)


Criteria & Outcome Measures

2012 revised International Chapel Hill Consensus Conference Nomenclature of Vasculitides.
(Arthritis Rheum. 2013;65:1-11.)

Preliminary classification criteria for the cryoglobulinaemic vasculitis.
(Ann Rheum Dis. 2011;70:1183-90.)

International Study Group Criteria for Diagnosis of Behcet’s Disease
(Lancet. 1990;335:1078-80.)

International Criteria for Behçet's Disease
(J Eur Acad Dermatol Venereol. 2014;28:338-47.)

Development and validation of a consensus methodology for the classification of the ANCA-associated vasculitides and polyarteritis nodosa for epidemiological studies
(Ann Rheum Dis 2007;66:222-7)

ACR/EULAR diagnosis and classification criteria in vasculitis study (DCVAS)

ACR 1990 classification criteria for GCA
(Arthritis Rheum. 1990;33:1122-8.)

The OMERACT core set of outcome measures for use in clinical trials of ANCA-associated vasculitis
(J Rheumatol 2011;38:1480-6)


Disease Scores & Online Calculators

Birmingham Vasculitis Activity Score (BVAS v.3)
(Ann Rheum Dis 2009;68:1827-32)

BVAS online calculator

Birmingham Vasculitis Activity Score – GPA
(Arthritis Rheum. 2001;44:912-20.);2-5/full

Five-Factor Score

Indian Takayasu Clinical Activity Score
(Rheumatology (Oxford). 2013;52:1795-801.)

Vasculitis Activity Index
(Arthritis Rheum 1999;42:2365–71);2-M/pdf

IgG4-Related Disease Responder Index
(Int J Rheumatol. 2012;2012:259408.)

BVAS and VDI training

The Vasculitis Damage Index
(Arthritis Rheum 1997;40:371-80)

The Combined Damage Assessment Index (CDA)
(Ann Rheum Dis. 2011;70:80-5)


Imaging Tools

Official site of the SONOgraphy on VASculitis (SONOVAS) study group with giant cell arteritis images database.



Vasculitis foundations
European Vasculitis Study Group (EUVAS)

Vasculitis Clinical Research Consortium