Recommendations and Guidelines

EULAR recommendations for the management of ANCA-associated vasculitis: 2022 update
(Ann Rheum Dis.2023 Mar 16;ard-2022-223764.)

EULAR/ERA-EDTA recommendations for the management of ANCA-associated vasculitis.
(Ann Rheum Dis. 2016;75:1583-94.)

CanVasc Recommendations for the Management of Antineutrophil Cytoplasm Antibody-associated Vasculitides.
(J Rheumatol. 2016;43:97-120.)

BSR and BHPR guideline for the management of adults with ANCA-associated vasculitis.
(Rheumatology (Oxford). 2014;53:2306-9.)

Eosinophilic granulomatosis with polyangiitis (Churg-Strauss) (EGPA) Consensus Task Force recommendations for evaluation and management.
(Eur J Intern Med. 2015;26:545-53.)

Management of giant cell arteritis: Recommendations of the French Study Group for Large Vessel Vasculitis (GEFA).
(Rev Med Interne. 2016;37:154-65.)

Management of Polymyalgia Rheumatica: 2015 Recommendations for the Management of Polymyalgia Rheumatica A European League Against Rheumatism/American College of Rheumatology Collaborative Initiative
(Arthritis Rheum. 2015;67:2569-80.)


BSR and BHPR guidelines for the management of giant cell arteritis.
(Rheumatology (Oxford). 2010;49:1594-7.)

EULAR recommendations for the management of large vessel vasculitis.
(Ann Rheum Dis. 2009;68:318-23.)

EULAR recommendations for the management of Behçet disease.
(Ann Rheum Dis. 2008;67:1656-62.)

Criteria and Outcome Measures

2012 revised International Chapel Hill Consensus Conference Nomenclature of Vasculitides.
(Arthritis Rheum. 2013;65:1-11.)

Validation of the classification criteria for cryoglobulinaemic vasculitis 
(Rheumatology (Oxford). 2014;53:2209-13.)


International Study Group Criteria for Diagnosis of Behcet’s Disease
(Lancet. 1990;335:1078-80.)

International Criteria for Behçet's Disease
(J Eur Acad Dermatol Venereol. 2014;28:338-47.)

Development and validation of a consensus methodology for the classification of the ANCA-associated vasculitides and polyarteritis nodosa for epidemiological studies
(Ann Rheum Dis 2007;66:222-7)

Anti-neutrophil cytoplasm antibodies (ANCA): Recent methodological advances—Lead to new consensus recommendations for ANCA detection
(J Immunol Methods. 2018;456:1-6)

ACR/EULAR diagnosis and classification criteria in vasculitis study (DCVAS)

ACR 1990 classification criteria for GCA
(Arthritis Rheum. 1990;33:1122-8.)

The OMERACT core set of outcome measures for use in clinical trials of ANCA-associated vasculitis
(J Rheumatol 2011;38:1480-6)

Disease Scores and Online Calculators

Birmingham Vasculitis Activity Score (BVAS v.3)
(Ann Rheum Dis 2009;68:1827-32)

BVAS online calculator

Birmingham Vasculitis Activity Score – GPA
(Arthritis Rheum. 2001;44:912-20.);2-5/full

Five-Factor Score

Indian Takayasu Clinical Activity Score
(Rheumatology (Oxford). 2013;52:1795-801.)

Vasculitis Activity Index
(Arthritis Rheum 1999;42:2365–71);2-M/pdf

IgG4-Related Disease Responder Index
(Int J Rheumatol. 2012;2012:259408.)

BVAS and VDI training

The Vasculitis Damage Index
(Arthritis Rheum 1997;40:371-80)

The Combined Damage Assessment Index (CDA)
(Ann Rheum Dis. 2011;70:80-5)

Imaging Tools

Official site of the SONOgraphy on VASculitis (SONOVAS) study group with giant cell arteritis images database.

Organisations and further links 

Vasculitis foundations
European Vasculitis Study Group (EUVAS)

Vasculitis Clinical Research Consortium